Project 460121

The contribution of CCN proteins to scleroderma fibrosis: cellular and molecular mechanisms

460121

The contribution of CCN proteins to scleroderma fibrosis: cellular and molecular mechanisms

$1,044,226
Project Information
Study Type: Unclear
Research Theme: Biomedical
Institution & Funding
Principal Investigator(s): Leask, Andrew C
Co-Investigator(s): Aslam, Muhammad N; Postovit, Lynne-Marie; Riser, Bruce L
Institution: University of Saskatchewan
CIHR Institute: Musculoskeletal Health and Arthritis
Program: Project Grant
Peer Review Committee: Cell Biology - Disease
Competition Year: 2022
Term: 5 yrs 0 mth
Abstract Summary

Fibrotic diseases such as scleroderma have limited therapeutic options. These diseases are characterized by extensive scar tissue deposition. The cells (fibroblasts) within the scar are subject to enhanced tension due to the surrounding scar tissue. They also themselves are abnormal in that they exert excessive tension on the scar tissue. It is believed that this excessive tension is responsible for the maintenance of the scar. A protein called CCN2 is expressed specifically in scar tissue and promotes this tension. A related protein CCN3 is not found in scar tissue, but normally acts to inhibit CCN2. We want to test whether CCN3 and peptides derived from CCN3) can block or reverse scleroderma fibrosis. At the end of the funding period, we will design and initiate clinical trials with our peptides to see if we can block fibrosis clinically.

No special research characteristics identified

This project does not include any of the advanced research characteristics tracked in our database.

Keywords
Ccn Proteins Connective Tissue Fibrosis Matricellular Proteins Microenvironment Scleroderma